J-LSMS 2018 | Archive | Issues 1 to 4

JOURNAL OF THE LOUISIANA STATE MEDICAL SOCIETY

Clinical Presentation

Radiological Features

Pathological Features

Prognosis

• Intraventricular • Midline • MRI: T1 iso, T2 hyper

• Necrosis and cyst formation common • Diffuse synaptophysin reactivity • GFAP+ in ~ 50% of cases

• Higher recurrence rate • Requires adjuvant radiotherapy or radiosurgery

• Young patients • Headache • Features of raised ICP • Rarely, cognitive dysfunction, seizures, etc

Central Neurocytoma

• MRI- Isointense on T1, iso to hyperintense on T2 • Variable contract enhancement • Calcification ± • Heterogenous • MRI- Iso on T1 and Iso to hyper on T2 • Contrast enhancement + • Calcifications + • Ill-defined outline • Paramedian or assymetric • MRI: T1 iso to hypo, T2- Hyper • Contrast enhancement + • May show edema and mass effect • Contrast enhancement + • Heterogenous solid cystic • Calcifications +

• Glial tumor without neuronal component • GFAP+

• Recurrence occurs without total excision • Requires post of radiotherapy

• Any age • Headache • Features of raised ICP

Low grade astrocytoma

• Memory dysfunction (with involvement of fornix and corpus callosum)

• Perinuclear satellosis • Involves white matter • Larger and varied nuclei

• Recurrence occurs without total excision • Requires post of radiotherapy

• Middle aged • Raised ICP due to hydrocephalus

Oligodendroglioma

• Large polygonal cells resembling astrocytes or ganglion cells • Perivascular pseudorosette • No neurons • Glial tumor cells in clusters in an abundant fibrillary matrix • No mature neurons • Intratumoral rosental fibres • Eosinophillic granular bodies • Glial cells without mature neurons • Glial cells major cell type • Perivascular lymphocytic infiltration • May show atypia • GFAP+ • Neoplastic ganglion and glial cells in reticulin network

• Good prognosis with rare recurrence • Adjucant therapy usually not required with total excision

• In children and yong adult • Male preponderence • Seizure is the most common presentation

Ganglioglioma

• Mixed solid cystic • Typical lesion is

• Complete resection carries good prognosis • Radiotherapy needed for incomplete resections

• Young children • Headache • Raised ICP due to hydrocephalus

Pilocytic astrocytoma

• Wall of lateral ventricle near foramen of Monro • MRI- T1 hypo and T2 hyper • Homogenous contrast enhancement characterized by a cystic lesion with mural nodule that enhances with contract • Midline location • Heterogenous with cystic areas • Lobulated apprance • T1 hypo and T2 hyper • Minimal contrast enhancement in septum pellucidum lesions

• Young age • Associated with tuberous sclerosis • Present with raised ICP due to HCP • Middle aged and elderly males • More common in 4 th ventricle • Present with raised ICP due to HCP

• Total excision leads to cure • Recurrence rare • Radiotherapy not needed • Total excision leads to cure • Recurrence rare • Radiotherapy not needed

Subependymal Giant cell astrocytoma

Subependymoma

• Young age • Seizures, headache • Raised ICP due to HCP

• Midline location • Homogenous

• Small round oligodendroglia like cells with floating neurons • Microcystic or alvelolar pattern • May express synaptophysic but not GFAP

• Excellent prognosis • Rare recurrence even if in subtotal excision • Radiotherapy not needed

Dysembroplastic neuroepithelial tumor

• T1 hypo, T2 hyperintense • Does not enhance with contrast • Higher ADC value

Table 2: Differentiating features of various tumors of septum pellucidum

J La State Med Soc VOL 170 JANUARY/FEBRUARY 2018 13

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